Omental caking: a rare manifestation of malignant peripheral nerve sheath tumour.

نویسندگان

  • Sadia Rizvi
  • Javed Mehboob
  • Asghar H Asghar
  • Ahmed Mateen
  • Tehseen Raza
  • Abid Hameed
چکیده

Malignant peripheral nerve sheath tumour (MPNST) is a very rare tumour with an incidence of one per 100,000 and constitutes between 3 to 10% of all soft tissue sarcomas. Most of the sarcoma involve the extremities and retroperitoneal regions. However, this case presented with mass in left inguinal region and then spread rapidly to omentum, assuming the appearance of an omental cake. Mass responded well to chemotherapy comprising of Ifosfamide and Doxorubicin.

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عنوان ژورنال:
  • Journal of the College of Physicians and Surgeons--Pakistan : JCPSP

دوره 20 8  شماره 

صفحات  -

تاریخ انتشار 2010